Alphabetical index of conditions
Condition |
Evidence level |
Chapter |
Acquired coagulation factor inhibitors (alloantibodies and autoantibodies), including acquired haemophilia, acquired von Willebrand syndrome, inhibitors to FVIII in haemophilia A, and inhibitors to FIX in haemophilia B (see coagulation factor inhibitors) |
|
|
Acquired hypogammaglobulinaemia secondary to haematological malignancies (chronic lymphocytic leukaemia, multiple myeloma, non-Hodgkin lymphoma, and other relevant malignancies and post- haemopoietic stem cell transplantation) |
2a |
5 |
Acute autonomic neuropathy (see Guillain–Barré syndrome) |
|
|
Acute disseminated encephalomyelitis |
2a |
6 |
Acute inflammatory demyelinating polyneuropathy
(see Guillain–Barré syndrome) |
|
|
Acute leukaemia in children |
2a |
7 |
Acute motor axonal neuropathy (see Guillain–Barré syndrome) |
|
|
Acute motor sensory axonal neuropathy (see Guillain–Barré syndrome) |
|
|
Acute optic neuritis |
2b |
8 |
Acute rheumatic fever |
2b |
8 |
Adrenoleukodystrophy |
4b |
8 |
Amegakaryocytic thrombocytopenia |
4b |
8 |
Amyotrophic lateral sclerosis
(see motor neuron disease) |
|
|
ANCA-positive systemic necrotising vasculitis |
2a |
6 |
Antiphospholipid syndrome — non-obstetric |
4b |
8 |
Aplastic anaemia/pancytopenia |
4b |
8 |
Asthma |
2c |
8 |
Atopic dermatitis/eczema (adult) |
2b |
8 |
Autism |
4b |
8 |
Autoimmune congenital heart block (neonatal lupus) |
4a |
7 |
Autoimmune haemolytic anaemia |
4a |
6 |
Autoimmune haemolytic anaemia with immune thrombocytopenia
(see Evans syndrome) |
|
|
Autoimmune neutropenia |
4a |
7 |
Autoimmune uveitis |
4a |
7 |
Autologous haemopoietic stem cell transplantation |
2c |
8 |
Behçet’s disease |
4b |
8 |
Bickerstaff’s brainstem encephalitis
(see Guillain–Barré syndrome) |
|
|
Bullous pemphigoid |
4a |
6 |
Capillary leak syndrome (see Systemic capillary leak syndrome) |
|
|
Cardiac failure — congestive |
2a |
8 |
Cardiac surgery with bypass — prophylaxis |
2a |
8 |
Cataplexy (see narcolepsy) |
|
|
Catastrophic antiphospholipid syndrome |
4a |
7 |
Chronic inflammatory demyelinating polyneuropathy (CIDP) |
1 |
5 |
Cicatricial pemphigoid |
2a |
6 |
Coagulation factor inhibitors (alloantibodies
and autoantibodies) — including acquired haemophilia, acquired von Willebrand syndrome, inhibitors to FVIII in haemophilia A, and inhibitors to FIX in haemophilia B |
2a |
7 |
Common variable immunodeficiency (CVID) (see primary immunodeficiency) |
|
|
Congenital heart block
(see autoimmune congenital heart block) |
|
|
Congestive cardiac failure |
2a |
8 |
Crohn’s disease |
4b |
8 |
Dermatitis/eczema atopic (adult)
(see atopic dermatitis/eczema) |
|
|
Demyelinating polyneuropathy (see chronic inflammatory) |
|
|
Dermatomyositis (see inflammatory myopathies) |
|
|
Devic disease (neuromyelitis optica) |
4a |
7 |
Diabetic amyotrophy |
4a |
7 |
Diabetic lumbosacral radiculoplexus neuropathy (See diabetic amyotrophy) |
|
|
Diabetic proximal neuropathy
(See diabetic amyotrophy) |
|
|
Diamond Blackfan syndrome |
4b |
8 |
Eczema, atopic dermatitis (adult)
(see atopic dermatitis/eczema) |
|
|
Encephalomyelitis - acute disseminated (see acute disseminated) |
|
|
Encephalopathy (see Hashimoto) |
|
|
Encephalopathy
(see limbic - nonparaneoplastic) |
|
|
Encephalopathy
(see limbic - paraneoplastic) |
|
|
Encephalopathy (see potassium channel) |
|
|
Epidermolysis bullosa acquisita |
4a |
7 |
Epilepsy — rare childhood cases |
2a |
7 |
Evans syndrome - autoimmune haemolytic anaemia with immune thrombocytopenia |
4a |
6 |
Female infertility |
4a |
8 |
Foeto-maternal/neonatal alloimmune thrombocytopenia (FMAIT/NAIT) |
4a |
6 |
Glomerulonephritis - IgA nephritis |
2b |
|
Glomerulonephritis (see lupus nephritis) |
|
8 |
Graves ophthalmopathy |
2a |
7 |
Guillain–Barré syndrome (GBS) |
1 |
5 |
Haemolytic anaemia
(see autoimmune haemolytic anaemia) |
|
|
Haemolytic anaemia — autoimmune with immune thrombocytopenia
(see Evans syndrome) |
|
|
Haemolytic disease of the newborn |
4a |
7 |
Haemolytic transfusion reaction |
4a |
7 |
Haemolytic uraemic syndrome |
4b |
8 |
Haemophagocytic syndrome |
4a |
6 |
Haemopoietic stem cell transplant
(see autologous) |
|
|
Hashimoto encephalopathy |
4a |
7 |
Heart block (see autoimmune congenital) |
|
|
Henoch–Schonlein purpura |
4b |
8 |
HIV/AIDS — adult |
2b |
8 |
HIV/AIDS — children |
2a |
7 |
Iatrogenic immunodeficiency
(see secondary hypogammaglobulinaemia) |
|
|
Idiopathic dilated cardiomyopathy |
2b |
8 |
Idiopathic thrombocytopenic purpura (ITP) — adults |
2a |
5 |
Idiopathic thrombocytopenic purpura (ITP) — child |
1 |
6 |
IgA nephritis (see glomerulonephritis) |
|
|
IgG subclass deficiency
(see specific antibody deficiency) |
|
|
IgM paraproteinaemic neuropathy |
2c |
6 |
Inclusion body myositis
(see inflammatory myopathies) |
|
|
Inflammatory myopathies
(polymyositis, dermatomyositis, inclusion body myositis) |
2a |
5 |
Inhibitors — coagulation factor (alloantibodies and autoantibodies), including acquired haemophilia, acquired von Willebrand syndrome, inhibitors to FVIII in haemophilia A, and inhibitors to FIX in haemophilia B (see coagulation factors inhibitors) |
|
|
Kawasaki disease |
1 |
5 |
Kidney transplantation |
1 |
6 |
Lambert–Eaton myasthenic syndrome |
2a |
5 |
Landau–Keffner syndrome (see Epilepsy) |
|
|
Lennox–Gastaut syndrome (see Epilepsy) |
|
|
Leukaemia in children (see acute leukaemia in children) |
|
|
Lewis-Sumner syndrome variant (see Guillain–Barré syndrome) |
|
|
Limbic encephalitis, nonparaneoplastic |
4a |
7 |
Limbic encephalitis, paraneoplastic |
4a |
7 |
Linear IgA disease |
4b |
8 |
Lupus cerebritis |
4a |
8 |
Lupus nephritis |
2a |
8 |
Lyell syndrome (see Toxic epidermal necrolysis) |
|
|
Miller Fisher syndrome (see Guillain–Barré syndrome) |
|
|
Moersch-Woltman syndrome (see Stiff person syndrome) |
|
|
Motor neuron disease/amyotrophic lateral sclerosis |
4b |
8 |
Mucocutaneous lymph node syndrome (see Kawasaki Disease) |
|
|
Mucous membrane pemphigoid
(see cicatricial pemphigoid) |
|
|
Multifocal motor neuropathy |
1 |
5 |
Multiple sclerosis |
2a |
6 |
Myalgic encephalomyelitis
|
2c |
8 |
Myasthenia gravis
|
1 |
5 |
Myocarditis in children
|
4a |
7 |
Narcolepsy/cataplexy
|
4a |
8 |
Neonatal alloimmune thrombocytopenia (NAIT) (see Foeto-maternal)
|
|
|
Neonatal haemochromatosis
|
2a |
5 |
Neonatal lupus
(see autoimmune congenital heart block)
|
|
|
Nephrotic syndrome
|
2a |
8 |
Neuromyelitis optica (see Devic disease)
|
|
|
Neuropathy
(see Chronic inflammatory demyelinating)
|
|
|
Neuropathy (see diabetic amyotrophy)
|
|
|
Neuropathy (see diabetic amyotrophy)
|
|
|
Neuropathy (see multifocal motor)
|
|
|
Neuropathy
(see paraneoplastic subacute sensory)
|
|
|
Neuropathy
(see polyneuropathy of critical illness)
|
|
|
Neutropenia (see autoimmune neutropenia)
|
|
|
Obsessive compulsive disorders
|
4a |
8 |
Opsoclonus-myoclonus ataxia
|
4a |
6 |
Optic neuritis (see acute optic neuritis)
|
|
|
Paediatric autoimmune neuropsychiatric
disorder associated with streptococcal infections (PANDAS)
|
2a |
7 |
Pancytopenia (see aplastic anaemia)
|
|
|
Paraneoplastic cerebellar degeneration
|
4a |
7 |
Paraneoplastic limbic encephalitis
(see limbic encephalitis – paraneoplastic)
|
|
|
Paraneoplastic neurological syndromes (see paraneoplastic subacute sensory neuropathy, Paraneoplastic cerebellar degeneration, limbic encephalitis paraneoplastic)
|
|
|
Paraneoplastic subacute sensory neuropathy
|
4a |
7 |
Pemphigus foliaceus
|
4a |
6 |
Pemphigus vulgaris
|
2a |
6 |
Polymyositis (see inflammatory myopathies)
|
|
|
Polyneuropathy of critical illness
|
4a |
8 |
Post-transfusion purpura
|
4a |
6 |
Potassium channel antibody-associated encephalopathy
|
4a |
7 |
Primary immunodeficiency diseases with antibody deficiency
|
2a |
5 |
Pure red cell aplasia
|
4b |
7 |
Pure white cell aplasia
|
4b |
7 |
Pyoderma gangrenosum
|
4a |
7 |
Rasmussen syndrome
|
2a |
7 |
Recurrent foetal loss
(with or without antiphospholipid syndrome)
|
3 |
8 |
Renal transplantation
(see kidney transplantation)
|
|
|
Rheumatic fever (see acute rheumatic fever)
|
|
|
Rheumatoid arthritis
|
2c |
8 |
Scleromyxedema
|
4a |
7 |
Secondary hypogammaglobulinaemia (including iatrogenic immunodeficiency)
|
4b |
6 |
Sepsis
|
2a |
8 |
Sickle cell disease
|
4b |
8 |
Sjogren's syndrome
|
4a |
7 |
Solid organ transplantation
(other than kidney)
|
4a |
7 |
Specific antibody deficiency
|
4a |
6 |
Steroid-responsive encephalopathy associated with autoimmune thyroiditis
(see Hashimoto)
|
|
|
Stevens–Johnson syndrome
(see toxic epidermal necrolysis/SJS)
|
|
|
Stiff person syndrome
|
2a |
5 |
Susac syndrome
|
4a |
7 |
Systemic capillary leak syndrome
|
4a |
7 |
Systemic lupus erythematosus (SLE)
|
2a |
8 |
Systemic necrotising vasculitis (see ANCA- positive systemic necrotising vasculitis)
|
|
|
Thrombocytopenia (see amegakaryocytic)
|
|
|
Thrombocytopenia (see Evans syndrome)
|
|
|
Thrombocytopenia
(see idiopathic thrombocytopenia purpura)
|
|
|
Thrombocytopenia (see neonatal alloimmune thrombocytopenia)
|
|
|
Thrombocytopenia
(see post-transfusion purpura)
|
|
|
Transient hypogammaglobulinaemia of infancy (see see primary immunodeficiency disease)
|
|
|
Toxic epidermal necrolysis/Stevens– Johnson syndrome (TEN/SJS)
|
4a |
6 |
Toxic shock syndrome
|
4a |
6 |
Ulcerative colitis
|
4b |
8 |
Uveitis (see autoimmune uveitis)
|
|
|
Wiskott–Aldrich syndrome (see see primary immunodeficiency disease)
|
|
|
X-linked agammaglobulinaemia
(see see primary immunodeficiency disease)
|
|
|