Criteria for the clinical use of Intravenous Immunoglobulin in Australia - Second Edition

Index of conditions

Chapter 5 : Conditions for which IVIg has an established therapeutic role

Conditions for which IVIg has an established therapeutic role
Condition
Acquired hypogammaglobulinaemia secondary to haematological malignancies
Chronic inflammatory demyelinating polyneuropathy
Guillain–Barré syndrome
Idiopathic (autoimmune) thrombocytopenia purpura (ITP) in adults
Inflammatory myopathies
Kawasaki disease
Lambert–Eaton myasthenic syndrome
Multifocal motor neuropathy
Myasthenia gravis
Neonatal haemochromatosis
Primary immunodeficiency diseases
Stiff person syndrome

Chapter 6 : Conditions for which IVIg has an emerging therapeutic role

Conditions for which IVIg has an emerging therapeutic role
Condition
Acute disseminated encephalomyelitis
ANCA-positive systemic necrotising vasculitis
Autoimmune haemolytic anaemia
Bullous pemphigoid
Cicatricial pemphigoid
Evans syndrome - autoimmune haemolytic anaemia with immune thrombocytopenia
Foeto-maternal/neonatal alloimmune thrombocytopenia
Haemophagocytic syndrome
Idiopathic (autoimmune) thrombocytopenia purpura (ITP) in children
IgM paraproteinaemic neuropathy
Kidney transplantation
Multiple sclerosis
Opsoclonus myoclonus ataxia
Pemphigus foliaceus
Pemphigus vulgaris
Post-transfusion purpura
Secondary hypogammaglobulinaemia (including iatrogenic immunodeficiency)
Specific antibody deficiency (including IgG subclasses)
Toxic epidermal necrolysis/Stevens–Johnson syndrome
Toxic shock syndrome

Chapter 7 : Conditions for which IVIg use is in exceptional circumstances only

Conditions for which IVIg use is in exceptional circumstances only
Condition
Acute leukaemia in children
Autoimmune congenital heart block
Autoimmune neutropenia
Autoimmune uveitis
Catastrophic antiphospholipid syndrome
Coagulation factor inhibitors
Devic disease
Diabetic amyotrophy
Epidermolysis bullosa acquisita
Epilepsy
Graves ophthalmopathy
Haemolytic disease of the newborn
Haemolytic transfusion reaction
Hashimoto encephalopathy
HIV in children
Limbic encephalitis, nonparaneoplastic
Myocarditis in children
Paediatric autoimmune neuropsychiatric disorder associated with streptococcal infections
Paraneoplastic syndromes: subacute sensory neuropathy, cerebellar degeneration, limbic encephalitis
Potassium channel antibody-associated encephalopathy
Pure red cell aplasia
Pure white cell aplasia
Pyoderma gangrenosum
Rasmussen syndrome
Scleromyxedema
Sjogren’s syndrome
Solid organ transplantation (other than kidney)
Susac syndrome
Systemic capillary leak syndrome

Chapter 8 : Conditions for which IVIg use is not supported

Conditions for which IVIg use is not supported
Condition
Acute optic neuritis
Acute rheumatic fever
Adrenoleukodystrophy
Amegakaryocytic thrombocytopenia
Antiphospholipid syndrome (non-obstetric)
Aplastic anaemia/pancytopenia
Asthma
Atopic dermatitis/eczema — adult
Autism
Autologous haemopoietic stem cell transplantation
Behçet’s disease
Cardiac surgery with bypass — prophylaxis
Congestive cardiac failure
Crohn’s disease
Diamond Blackfan syndrome
Female infertility
Glomerulonephritis — IgA nephritis
Haemolytic uraemic syndrome
Henoch–Schonlein purpura
HIV/AIDS — adult
Idiopathic dilated cardiomyopathy
Linear IgA disease
Lupus cerebritis
Lupus nephritis
Motor neuron disease/amyotrophic lateral sclerosis
Myalgic encephalomyelitis
Narcolepsy/cataplexy
Nephrotic syndrome
Obsessive compulsive disorders
Polyneuropathy of critical illness
Recurrent foetal loss (with or without antiphospholipid syndrome)
Rheumatoid arthritis
Sepsis
Sickle cell disease
Systemic lupus erythematosus
Ulcerative colitis